产品编号:I780750
产品规格:1g
产品价格:面议
| 标准品编号: | I780750 |
| 名称: | N-Isobutyrylglycine |
| 别名: | N-(2-methyl-1-oxopropyl)glycine; N-Isobutyrylglycine; |
| CAS号: | 15926-18-8 |
| 分子式: | C₆H₁₁NO₃ |
| 外观: | 白色固体 |
| 熔点: | 100-104°C |
| 分子量: | 145.16 |
| 储存: | 冰箱 |
| 溶解度: | DMSO, Methanol |
| 种类: | Building Blocks; Amino Acids; Pharmaceutical/API Drug Impurities/Metabolites; |
| 应用: | N-Isobutyrylglycine detection is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isobutyrylglycine detection is also used in the diagnosis of isobutyryl-CoA dehydrogenase deficiency. |
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