L-Cysteine-D-penicillamine Disulfide

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产品编号:C996800

产品规格:250mg

产品价格:面议


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标准品编号: C996800
名称: L-Cysteine-D-penicillamine Disulfide
别名: 3-[[(2R)-2-Amino-2-carboxyethyl]dithio]-D-valine; 3,3-Dimethyl-3,3'-dithiodialanine; (R)-3-[(2-Amino-2-carboxyethyl)dithio]-D-valine; 3-[(L-2-Amino-2-carboxyethyl)dithio]-D-valine; Penicillamine Cysteine Disulfide;
CAS号: 18840-45-4
分子式: C₈H₁₆N₂O₄S₂
外观: 白色固体
熔点: >175°C (dec.)
分子量: 268.35
储存: Hygroscopic, -20°C Freezer, Under inert atmosphere
溶解性: Water (Slightly, Sonicated)
稳定性: Hygroscopic
种类: Standards; Amino Acids;
应用: L-Cysteine-D-penicillamine Disulfide is the major urinary metabolite of D-Penicillamine (P223000). L-Cysteine-D-penicillamine Disulfide exposure induces vacuolation in cultured fibroblasts from individuals with cystinosis.
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